Myxoid Liposarcoma of the Skin-Rare Case with Multifocal Presentation

Abstract

The dermis is an exceptionally rare primary site of presentation of liposarcomas. Only two cases of the myxoidvariety have been reported in the literature. The lesions present as dome shaped or polypoidal masses thatfrequently show high grade morphological changes, but carry a comparitively a good prognosis. We report a 35 yearold male who presented with multiple "ginger tuber" like lesions on the upper half of the body. The clinical behaviourwas extremely aggressive with a short history of short duration.It is important to recognise the fact that thoughdermal liposarcomas by and large carry a good prognosis there exists a rare subset with a "multifocal" presentationthat suggests a poor clinical course even though the histopathological features may show a high grade pathologysuggesting a good prognosis. These cases require urgent treatment with radiotherapy and chemotherapy, wheresurgery may have no role in therapeutics. It is for this reason that we are presenting this rare subset of “multifocalmyxoid dermal liposarcoma” which should alert all clinicians to act with speed.